Netherton Syndrome is a severe autosomal recessive disease characterized by congenital
erythroderma, bamboo hair and abnormality in the immune system.
Netherton Syndrome is a severe autosomal recessive disease characterized by congenital
erythroderma, "bamboo hair" and abnormality in the immune system.
In addition, patients may have
erythroderma with desquamation.
Lamellar ichthyosis generally occurs at birth with a striking collodion-type membrane covering the body and underlying
erythroderma, which then desquamates.
In 2014 she was treated with narrow-band UVB, which had to be terminated after 20 sessions due to exacerbation and progression to
erythroderma. In June 2014, cyclosporine A was introduced with only a temporary effect, and there was a gradual increase of IgE (8,058 IU/ml in June 2015, and 41,445 and 48,526 in October and December 2015, respectively).
Berth-Jones J, Eczema, Lichenification, Prurigo and
Erythroderma. In: Burns T, Breathnach S, Cox N, Griffiths C, eds.
Erythroderma or exfoliative dermatitis is any inflammatory skin disease that affects more than 90% of the body surface.
On physical examination, the patient had diffuse,
erythroderma and abdominal tenderness.
Most patients with HLH and cutaneous findings present with nonspecific maculopapular eruption, purpura,
erythroderma, and edema (9).
Skin findings vary from maculopapular rash to
erythroderma.
We report a case of psoriasis-form
erythroderma induced by HCQ in an SLE patient.
(17,18,19,20) Dermatologic side effects include urticaria, morbilliform and vesiculobullous eruptions, exfoliative
erythroderma, erythema multiforme, Steven Johnson syndrome and toxic epidermal necrosis.